SOME GLYCOGEN STORAGE DISORDERS
|
Type |
Name |
Enzyme deficient |
|
Type - I Type - II Type - III Type - IV Type - V Type - VI |
Von Gierke's disease Pompe's disease Limit dextrinosis Amylopectinosis Mc Ardle's syndrome Her's disease |
Glucose-6-phosphotase Lysomal alpha-1-4 and -1; 6-glycosides Debranching enzyme Branching enzyme Muscle phosphorylase Liver phosphorylase |
